Paucity of biliary ducts: A rare etiology of neonatal cholestasis

Authors

  • Steven Cornell Figiel
  • Arie Franco
  • Darko Pucar
  • Kristopher Neal Lewis
  • Jeffrey Roberts Lee

DOI:

https://doi.org/10.3941/jrcr.v6i2.892

Keywords:

Alagille syndrome, Cholestasis, Biliary ducts

Abstract

We report a case of a newborn with cholestasis that was diagnosed as nonsyndromic Alagille syndrome. The main feature of the disease is a paucity of biliary ducts. There are two known types of the disease: the syndromic type which is associated with other congenital defects and the nonsyndromic type without other anomalies detected at birth. We describe the case and discuss its clinical and radiologic findings. We also discuss the various etiologies of cholestasis that are included in the differential diagnosis.

Author Biographies

Steven Cornell Figiel

Department of Radiology

Arie Franco

Department of Radiology

Darko Pucar

Department of Radiology

Kristopher Neal Lewis

Department of Radiology

Jeffrey Roberts Lee

Department of Pathology
Journal of Radiology Case Reports February 2012 issue - MRgFUS treatment of uterine fibroid in a nulliparous woman with acute retention of urine by Nyapathy et al.

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Published

2012-02-14

Issue

Vol. 6 No. 2 (2012)

Section

Pediatric Radiology

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