Uterus didelphys with unilateral distal vaginal agenesis and ipsilateral renal agenesis: Common presentation of an unusual variation

Authors

  • Luther Adair II
  • Maria Georgiades
  • Rhonda Osborne
  • Tsz Ng

DOI:

https://doi.org/10.3941/jrcr.v5i1.572

Keywords:

didelphys, uterine, unilateral, vaginal agenesis, ipsilateral renal agenesis

Abstract

Mullerian duct abnormalities are congenital malformations that are easily missed and can lead to incorrect diagnosis and further unnecessary operative procedures.  In this case, a young female presented with cyclic pelvic pain that continued after previous surgical resection of an ovarian cyst. Further investigation with clinical examinations and multimodality imaging demonstrated ipsilateral renal agenesis and a Class III Mullerian duct anomaly (MDA) requiring a second operative procedure.  It is believed that this case is a variant of the described obstructed hemi-vagina with ipsilateral renal agenesis (OVIRA) anomaly as pathologically there was ipsilateral renal agenesis and complete vaginal agenesis in our case.   It is imperative to have a high clinical suspicion of mullerian duct abnormalities when encountering a patient with other urogenital anomalies. This will decrease the amount of misdiagnoses, guide appropriate surgical intervention, and decrease the risk of future reproductive complications.

Author Biographies

Luther Adair II

<

Maria Georgiades

Department of Surgery

Surgery Resident PGY-3

Rhonda Osborne

Department of Radiology

Attending Radiologist

 

Tsz Ng

Department of Radiology

Attending Radiologist

Published

2011-01-22

Issue

Section

Obstetric & Gynecologic Radiology