Duplicated Pelvic Floor Musculature and Diastematomyelia in a Cloacal Exstrophy Patient

Authors

  • Brian Masao Inouye
  • Ali Tourchi
  • Eric Z Massanyi
  • John P Gearhart
  • Aylin Tekes

DOI:

https://doi.org/10.3941/jrcr.v8i10.2088

Keywords:

Diastematomyelia, Spinal Dysraphism, Duplicated Pelvic Floor, Cloacal Exstrophy, Exstrophy-Epispadias Complex, Etiology

Abstract

Cloacal exstrophy is the most severe and rare form of the exstrophy-epispadias complex, presenting with exposed bladder halves extruding through an abdominal wall defect and variable genitourinary, gastrointestinal, musculoskeletal, and neurological defects. The authors report magnetic resonance imaging findings of a neurologically-intact, 24-month-old female with cloacal exstrophy who presented with anterior spinal dysraphism and diastematomyelia and duplicate pelvic floor musculature. The constellation of defects suggests a common genetic, biochemical, and embryological origin for duplication of the bladder, spinal cord, and pelvic floor muscles occurring in the fourth week of gestation.

Author Biographies

Brian Masao Inouye

James Buchanan Brady Urological Institute

The Johns Hopkins Children's Hospital

1800 Orleans Street

Suite 7302

Baltimore, MD 21287

Ali Tourchi

James Buchanan Brady Urological Institute

The Johns Hopkins Children's Hospital

Eric Z Massanyi

Northeast Ohio Medical University

Akron Children's Hospital

John P Gearhart

James Buchanan Brady Urological Institute

The Johns Hopkins Children's Hospital

Aylin Tekes

Johns Hopkins Hospital
The Russell H. Morgan Department of Radiology and Radiological Sciences
Division of Pediatric Radiology, Section of Pediatric Neuroradiology

1800 Orleans Street

Zayed 4th floor, Room 4155
Baltimore, MD 21287

Journal of Radiology Case Reports October 2014 issue - Cover page: Duplicated Pelvic Floor Musculature and Diastematomyelia in a Cloacal Exstrophy Patient by Brian M Inouye et al.

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Published

2014-10-19

Issue

Vol. 8 No. 10 (2014)

Section

Pediatric Radiology

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