Erdheim-Chester disease with rare radiological features in a 14-year old girl with pre-B Acute Lymphocytic Leukemia and Diabetes mellitus

Authors

  • Varanasi Venkata Rama Krishna
  • Teo Eu Leong Harvey James
  • Kenneth Tou En Chang
  • Soh Shui Yen

DOI:

https://doi.org/10.3941/jrcr.v8i8.1899

Keywords:

Erdheim-Chester disease, Langerhans cell histiocytosis, osteolytic lesions, Touton type giant cells, Interferon alpha

Abstract

We report a case of a 14 year-old girl with Diabetes Mellitus who was in remission with pre-B cell Acute Lymphoblastic Leukemia and subsequently diagnosed with Erdheim-Chester disease.  Erdheim-Chester disease is a non-Langerhans cell histiocytosis and is very rare in children.  In addition, the radiological features of the lesions are atypical and have not been reported in children.  There is no known association between the three conditions and this is the first reported case in the literature.  A literature review of Erdheim-Chester disease will be performed.
Journal of Radiology Case Reports August 2014 issue - Cover page: Transarterial Embolization of a Hepatic Arteriovenous Malformation in an Infant Using Onyx: A Case Report and Review of the Differential Diagnosis Imaging Findings by Christopher Bolus et a

Downloads

Published

2014-08-25

Issue

Vol. 8 No. 8 (2014)

Section

Pediatric Radiology

License

The publisher holds the copyright to the published articles and contents. However, the articles in this journal are open-access articles distributed under the terms of the Creative Commons Attribution-NonCommercial-NoDerivs 4.0 License, which permits reproduction and distribution, provided the original work is properly cited. The publisher and author have the right to use the text, images and other multimedia contents from the submitted work for further usage in affiliated programs. Commercial use and derivative works are not permitted, unless explicitly allowed by the publisher.