Large leiomyoma in a woman with Mayer-Rokitansky-Kuster-Hauser syndrome

Authors

  • KISHAN SINGH RAWAT
  • Tarvinder Buxi
  • Anurag Yadav
  • Samarjit S Ghuman
  • Shashi Dhawan

DOI:

https://doi.org/10.3941/jrcr.v7i3.1267

Keywords:

MRKH syndrome, mullerian duct anomalies, leiomyoma, cystic degeneration

Abstract

Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a rare congenital anomaly characterized as aplasia or hypoplasia of uterus and vagina in women with normal development of secondary sex characteristics. It affects 1 in 4000-5000 female births. Women with this syndrome present with primary amenorrhoea. MRKH syndrome may be associated with renal, skeletal, cardiac and auditory anomalies. Women with MRKH syndrome may develop leiomyoma from a rudimentary uterus, though very rare. Initial investigation in women having MRKH syndrome with leiomyoma is ultrasonography (USG). However, CT and MRI are more accurate to evaluate the pelvic anatomy and pathologies.
Journal of Radiology Case Reports March 2013 issue - Cover page: Tracheobronchopathia Osteochondroplastica - A rare or an overlooked entity? by Shikha Jindal et al.

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Published

2013-03-11

Issue

Vol. 7 No. 3 (2013)

Section

Obstetric & Gynecologic Radiology

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