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Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a rare congenital anomaly characterized by a triad of markedly dilated non-obstructed urinary bladder, microcolon and decreased or absent intestinal peristalsis. Diagnosis is made with pre- or postnatal abdominal US and/or MRI. The radiologist should be aware of the possibility of unusual presentation of air filled bladder, ureters and pelvicalyces in this syndrome.






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An Unusual Urinary Tract Presentation in a Case of Megacystis Microcolon Intestinal Hypoperistalsis Syndrome

Free full text article: An Unusual Urinary Tract Presentation in a Case of Megacystis Microcolon Intestinal Hypoperistalsis Syndrome

Abstract
Megacystis microcolon intestinal hypoperistalsis syndrome is a rare congenital anomaly. Several pathogeneses have been described so far, but there is no single mechanism that can explain all the findings of the syndrome. Affected newborns usually present clinically in the first few days of life. The mainstay of diagnosis is a pre or a postnatal imaging evaluation using ultrasound or magnetic resonance imaging. We report an unusual urinary tract finding in a patient with the classic triads of the syndrome that was diagnosed with both pre and postnatal imaging evaluation.






References



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