Question:

Which of the following is false regarding the demographics of CPPD?
1. Very low incidence worldwide.
2. Ethnicity may have a role in incidence.
3. More common among the elderly.
4. More common in females.
5. Can be seen in children.





Answer:

The correct answer for the question "Which of the following is false regarding the demographics of CPPD?" is:

5. Can be seen in children.



Explanation
1. Very low incidence worldwide is true. [In the English language literature, only 35 patients from 14 different institutions have been reported].

2. Ethnicity may have a role is true. There may be a higher incidence in Asian countries. [However, Goto et al suggests that this entity may be more common than previously thought [15]. In their study, 40 patients out of 2023 studied demonstrated the clinical and radiological features to support the diagnosis of CDS (Crowned Dens Syndrome). Whether this may be related to the ethnicity of the patient population (the study was performed in Japan) will require further investigation.]

3. Common among the elderly is true. [More than two thirds of cases are found in patients older than 70 years of age and females are slightly more affected.]

4. More common in females is true. The male to female ratio is 0.6. [More than two thirds of cases are found in patients older than 70 years of age and females are slightly more affected.]

5. Can be seen in children is false. CPPD is a disease process of the elderly and has not been described in children.



From the manuscript:
CPPD Crowned Dens Syndrome with clivus destruction: A case report
Radiology Case. 2011 Aug; 5(8):30-37


This article belongs to the MSK section.




Bookmark and Share

From the manuscript

CPPD Crowned Dens Syndrome with clivus destruction: A case report

Free full text article: CPPD Crowned Dens Syndrome with clivus destruction: A case report

Abstract
We report a case of CPPD crowned dens syndrome in an 87 year white old male with a known history of pseudogout, with clinical and radiological features characteristic of this syndrome. Interestingly, there was significant mass effect on the clivus, with clivus erosion and destruction, a finding that has not previously been described with this syndrome. The clinical and radiological characteristics of Crowned Dens syndrome, as well as CPPD are reviewed. We suggest that CPPD crowned dens syndrome may be included in the differential diagnosis when clivus destruction or erosion, in association with a soft tissue mass with calcification, is seen.






References



1. Bouvet JP, le Parc JM, Michalski B, Benlahrache C, Anquier L. Acute neck pain due to calcifications surrounding the odontoid process: the crowned dens syndrome. Arthritis Rheum 1985;28:1417-20
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


2. Malca SA, Roche PH, Pellet W, Combalbert A. Crowned dens syndrome: a manifestation of hydroxy-apatite rheumatism. Acta Neurochir (Wien).1995;135:126-30
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


3. Aouba A, Vuillemin-Bodaghi V, Mutschler C, De Bandt M. Crowned dens syndrome misdiagnosed as polymyalgia rheumatica, giant cell arteritis, meningitis or spondylitis: an analysis of eight cases. Rheumatology.2004;43:1508-12
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


4. Wu DW, Reginato AJ, Torriani M, Robinson DR, Reginato AM. The crowned dens syndrome as a cause of neck pain: report of two new cases and review of the literature. Arthritis Rheum 2005;53:133-7
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


5. Baysal T, Baysal O, Kutlu R, Karaman I, Mizrak B. The crowned dens syndrome: a rare form of calcium pyrophosphate deposition disease. Eur Radiol 2000;10:1003-5
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


6. el-Khoury GY, Tozzi JE, Clark CR, Foucar E, Menezes AH, Smoker WR. Massive calcium pyrophosphate crystal deposition at the craniovertebral junction. AJR Am J Roentgenol 1985;145:777-8
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


7. Wells CR, Morgello S, DiCarlo E. Cervical myelopathy due to calcium pyrophosphate dihydrate deposition disease. J Neurol Neurosurg Psychiatry.1991;54:658-9
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


8. Wendling D. Syndrome de l`odontoide couronnee. Synoviale.1992;10:25-7.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


9. Alcalay M, Debiais F, Marco M, Wendling D, Tavernier Ch, Le Goff P, Le Parc JM. The crowned dens syndrome and apatite deposition disease. A sexlinked disease? Arthritis Rheum 1992;35:s212.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


10. Constantin A, Bouteiller G. Acute neck pain and fever as the first manifestation of chondrocalcinosis with calcification of the transverse ligament of the atlas. Five case-reports with a literature review Rev Rhum Engl Ed
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


12. Kobayashi Y, Mochida J, Saito I, Matui S, Toh E. Calcification of the alar ligament of the cervical spine: imaging findings and clinical course. Skeletal Radiol 2001;30:295-7
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


13. Sato Y, Yasuda T, Konno S, Kuwayama A, Komatsu K. Pseudogout showing meningoencephalitic symptoms: crowned dens syndrome. Intern Med 2004;43:865-8
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


14. Ritter J, Kerr LD, Valeriano-Marcet J, Spiera H. ACTH revisited: effective treatment for acute crystal induced synovitis in patients with multiple medical problems. J Rheumatol 1994;21:696-9
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


15. Goto S, Umehara J, Aizawa T, Kokubun S. Crowned Dens syndrome. J Bone Joint Surg Am 2007 Dec;89(12):2732-6
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


16. Saadeh C. Calcium Pyrophosphate Deposition Disease. Emedicine, September 2009 http://emedicine.medscape.com/article/330936-overview
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine




Search for articles with similar topics:

Keyword search:

1. Calcium pyrophosphate dihydrate deposition disease

2. dens

3. clivus


This article belongs to the MSK section.


Search for more in the Internet

Peer-reviewed Radiology Search




Discuss it!

Bookmark and Share




© Journal of Radiology Case Reports - The Interactive Radiology Journal
Affiliated journal of Radiolopolis - The International Radiology Community


The Journal of Radiology Case Reports