Question:

The following is false regarding idiopathic pulmonary haemosiderosis (IPH):
1. IPH is fatal if left untreated.
2. The prognosis is considered to be good.
3. The average survival rate is 2.5 years.
4. IPH is described as a triad of anaemia, haemoptysis and pulmonary infiltrate.
5. IPH can progress to lung fibrosis.





Answer:

The correct answer for the question "The following is false regarding idiopathic pulmonary haemosiderosis (IPH):" is:

2. The prognosis is considered to be good.



Explanation
a) IPH is fatal if left untreated [can be lethal if left untreated].

b) The prognosis of IPH is poor [the prognosis of IPH was considered to be poor].

c) The average survival rate is 2.5 years from the time of diagnosis [the prognosis of IPH was considered to be poor with average survival of 2.5 years after diagnosis].

d) IPH is described as a triad of anaemia, haemoptysis and pulmonary haemosiderosis [It was described first by Ceelen 1931 as a triad of haemoptysis, anaemia and pulmonary infiltrates].

e) It can progress to lung fibrosis if not treated [can be lethal if left untreated due to progressive pulmonary fibrosis].



From the manuscript:
Case Report of Idiopathic Pulmonary Haemosiderosis in a Child with recurrent chest infections
Radiology Case. 2011 Sep; 5(9):30-35


This article belongs to the Pediatric section.




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From the manuscript

Case Report of Idiopathic Pulmonary Haemosiderosis in a Child with recurrent chest infections

Free full text article: Case Report of Idiopathic Pulmonary Haemosiderosis in a Child with recurrent chest infections

Abstract
Idiopathic pulmonary haemosiderosis (IPH) is a rare condition that usually presents as a triad of haemoptysis, iron deficiency anaemia and pulmonary infiltrates. We report a case of IPH diagnosed in a 7 year old boy who had recurrent hospital admissions with severe chest infections and haemoptysis from his first few months of life. He was found to have microcytic hypochromic anaemia, diffuse infiltrate shadowing on his chest X-ray (CXR) and ground-glass opacification on his computed tomogram (CT). Perl`s Prussian blue staining of his bronchoalveolar lavage fluid revealed haemosiderin-laden macrophage infiltration. After exclusion of infective, cardiac, immunological and glomerular causes, he was diagnosed with idiopathic pulmonary haemosiderosis. He has since been treated intermittently with steroids, which have failed to control his symptoms fully.






References



1. Blanco A, Solis P, Gomez S, Valbuena C, Telleria JJ. Antineutrophil cytoplasmic antibodies (ANCA) in idiopathic pulmonary haemosiderosis. Pediatr Allergy Immunol 1994; 5: 235-9
Get full text
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2. Ceelen W. In: Handbuch der speziellen pathologischen Anatomie und Histologie. Eds F Henke & 0 Lubarsch
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


3. Soergel K, Sommers SC. Idiopathic pulmonary hemosiderosis and related syndromes. Am J Med 1962;32:499-511
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


4. Kjellman B, Elinder G, Garwicz S, Svan H. Idiopathic pulmonary haemosiderosis in Swedish children. Acta Paediatr Scand
Get full text
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5. Ohga S, Takahashi K, Miyazaki S, Kato H, Ueda K. Idiopathic pulmonary haemosiderosis in Japan: 39 possible cases from a survey questionnaire. Eur J
Get full text
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


6. Chen KC, Hsiao CC, Huang SC, Ko SF, Niu CK. Anaemia as the sole presenting symptom of idiopathic pulmonary haemosiderosis: report of two cases. Chang Gung Med J 2004; 27:824-9
Get full text
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7. Derbent M, Ozacay F, Saatci U, Ozbeck N. Severe iron deficiency anemia in achild with idiopathic pulmonary haemosiderosis: a case report. Turk J pediatr 2002;44:258-60
Get full text
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9. Elder J, Kirk G, Smith W. Idiopathic pulmonary haemosiderosis and the Good Pasture Syndrome. Report of 3 cases: British Medical Journal 1965,2,1152-1155
Get full text
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10. Leaker B, Cambridge G, R M du Bois, Neild G. Idiopathic pulmonary haemosiderosis: a form of microscopic polyarteritis? Thorax 1992;47:988-990.
Get full text
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11. Milman N, Pedersen FM. Idiopathic Pulmonary Haemosiderosis. Epidemiology, pathogenic aspects and diagnosis Respir
Get full text
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12.Tutor JD, Eid NS. Treatment of idiopathic pulmonary haemosiderosis with inhaled flunisolide.South Med J 1995;88:984-986. PMID: 7660222.
Get full text
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13. Saeed M, Woo M, MacLaughlin E, Margetis M, Keens T. Prognosis in Pediatric Idiopathic Pulmonary Hemosiderosis. Chest 1999;116:721-725
Get full text
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