Question:

The chest radiographic differentials for a case of isolated unilateral pulmonary artery agenesis include which of the following?
1. Swyer-James syndrome
2. Lobar atelectasis
3. Thymoma
4. Pulmonary artery hypoplasia
5. Lung agenesis/ hypoplasia complex





Answer:

The correct answers for the question "The chest radiographic differentials for a case of isolated unilateral pulmonary artery agenesis include which of the following?" are:

1. Swyer-James syndrome

2. Lobar atelectasis

4. Pulmonary artery hypoplasia

5. Lung agenesis/ hypoplasia complex



Explanation
The typical chest radiographic appearance of isolated unilateral absent pulmonary artery include a small hyperlucent hemithorax with a mediastinal shift to the affected side and elevation of the diaphragm, findings which can also be seen in Swyer-James syndrome, lobar atelectasis, post lobectomy status, lung agenesis/ hypoplasia complex, scimitar syndrome and agenesis/hypoplasia of the pulmonary artery.[The differentials include Swyer-James syndrome, lobar atelectasis, post lobectomy status, pulmonary agenesis/ hypoplasia complex and agenesis/hypoplasia of the pulmonary artery.]



From the manuscript:
Incidentally detected unilateral pulmonary artery agenesis with pulmonary hypoplasia in a 67 year old woman
Radiology Case. 2010 Nov; 4(11):32-37


This article belongs to the Chest section.




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From the manuscript

Incidentally detected unilateral pulmonary artery agenesis with pulmonary hypoplasia in a 67 year old woman

Free full text article: Incidentally detected unilateral pulmonary artery agenesis with pulmonary hypoplasia in a 67 year old woman

Abstract
Unilateral pulmonary artery agenesis is commonly seen associated with other congenital cardiovascular defects, when it is detected early in life, but isolated absence of the pulmonary artery is a rare entity, usually detected in adulthood. The latter patients are usually asymptomatic or might present with varied non-specific manifestations such as respiratory tract infections and hemoptysis. This report describes the imaging findings of a 67 year old female with absence of the right pulmonary artery. The embryology and clinical manifestations of the condition are reviewed.






References



1. Shostak E, Sarwar A. A 50-year-old woman with dyspnea, lower extremity edema, and volume loss of the right hemithorax. Chest 2009 Aug; 136(2): 628-32.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


2. Kadir IS, Thekudan J, Dheodar A, Jones MT, Carroll KB. Congenital unilateral pulmonary artery agenesis and aspergilloma. Ann Thorac Surg 2002 Dec; 74(6): 2169-71.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


3. Ten Harkel AD, Blom NA, Ottenkamp J. Isolated unilateral absence of a pulmonary artery: a case report and review of the literature. Chest 2002 Oct; 122(4): 1471-7.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


4. Bouros D, Pare P, Panagou P, Tsintiris K, Siafakas N. The varied manifestation of pulmonary artery agenesis in adulthood. Chest 1995 Sep; 108(3): 670-6.5 Nana-Sinkam P, Bost TW, Sippel JM
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


6. Apostolopoulou SC, Kelekis NL, Brountzos EN, Rammos S, Kelekis DA. "Absent" pulmonary artery in one adult and five pediatric patients: imaging, embryology, and therapeutic implications. AJR Am J Roentgenol 2002 Nov; 179(5): 1253-60.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


7. Welch K, Hanley F, Johnston T, Cailes C, Shah MJ. Isolated unilateral absence of right proximal pulmonary artery: surgical repair and follow-up. Ann Thorac Surg 2005 Apr; 79(4): 1399-402.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


8. Turner DR, Vincent JA, Epstein ML. Isolated right pulmonary artery discontinuity. Images Paediatr Cardiol 2000; 4(4): 24-30.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


9. Gupta K, Livesay JJ, Lufschanowski R. Absent right pulmonary artery with coronary collaterals supplying the affected lung. Circulation 2001 Jul 24; 104(4): E12-E13.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


10. Rousou AJ, Tetenta S, Boffa DJ. Pulmonary artery agenesis and Kommerell`s diverticulum presenting with hemoptysis. Eur J Cardiothorac Surg 2009 Feb; 35(2): 370-2.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine


11. Toews WH, Pappas G. Surgical management of absent right pulmonary artery with associated pulmonary hypertension. Chest 1983 Oct; 84(4): 497-9.
Find similar topics on Read this article on PubMed :: Find similar articles on Google scholarScholar :: Search for similar topics with the Radiology specific search engine Radiology search engine




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