Question:

Which of the following is seen in right Isomerism?
1. Piggy-backed IVC.
2. Double vessel sign.
3. Multiple spleens.
4. Female predilection.
5. Biliary atresia.





Answer:

The correct answer for the question "Which of the following is seen in right Isomerism?" is:

1. Piggy-backed IVC.



Explanation
1. Piggy-backed IVC.[Majority are characterised by bilateral superior vena cava draining into bilateral atria, both lungs with major and minor fissures, bilateral eparterial bronchi, complex cardiac anomalies, absent spleen, midline symmetrical liver with midline gall bladder, gut malrotation, piggy-back IVC, truncated pancreas.]

2. Double vessel sign.[Left Isomerism is seen more in females and is characterized by only major fissures in both lungs, bilateral hyparterial bronchi, congenital cardiac anomalies such as ASD and VSD, interrupted IVC with azygous continuation into thorax (the Double-vessel sign), multiple spleens, gut malrotation, biliary atresia. Most patients survive up to mid adolescence.]

3. Multiple spleens. [Left Isomerism is seen more in females and is characterized by only major fissures in both lungs, bilateral hyparterial bronchi, congenital cardiac anomalies such as ASD and VSD, interrupted IVC with azygous continuation into thorax (the Double-vessel sign), multiple spleens, gut malrotation, biliary atresia. Most patients survive up to mid adolescence.]

4. Female predilection. [Left Isomerism is seen more in females and is characterized by only major fissures in both lungs, bilateral hyparterial bronchi, congenital cardiac anomalies such as ASD and VSD, interrupted IVC with azygous continuation into thorax (the Double-vessel sign), multiple spleens, gut malrotation, biliary atresia. Most patients survive up to mid adolescence.]

5. Biliary atresia. [Left Isomerism is seen more in females and is characterized by only major fissures in both lungs, bilateral hyparterial bronchi, congenital cardiac anomalies such as ASD and VSD, interrupted IVC with azygous continuation into thorax (the Double-vessel sign), multiple spleens, gut malrotation, biliary atresia. Most patients survive up to mid adolescence.]



From the manuscript:
Right isomerism with complex cardiac anomalies presenting with dysphagia - A case report
Radiology Case. 2011 Apr; 5(4):1-9


This article belongs to the General section.




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From the manuscript

Right isomerism with complex cardiac anomalies presenting with dysphagia - A case report

Free full text article: Right isomerism with complex cardiac anomalies presenting with dysphagia - A case report

Abstract
Isomerism or Heterotaxy syndromes are rare multifaceted congenital anomalies with multi-system involvement. Grouped under the broad category of Situs Ambiguous defects, these often pose diagnostic difficulties due to their varied and confusing anatomy. Since patients rarely survive into adulthood due to cardiovascular complications, the etiology and natural history of such conditions are not fully understood. Imaging provides the most accurate non invasive method for diagnosis and thereby, prognosis in such cases. We present a case of right sided Isomerism with complex cardiac anomalies in a 17 year old adolescent, who presented with dysphagia as one of the main complaints. Multi modality imaging demonstrated the intricate abnormalities in vital systems.






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