Magnetic resonance imaging in Hirayama Disease

Authors

  • Maria Catalina Vargas
  • Mauricio Castlillo

DOI:

https://doi.org/10.3941/jrcr.v5i3.602

Keywords:

spinal cord compression, magnetic resonance imaging, spinal muscular atrophy

Abstract

Hirayama disease (HD) is a rare type of cervical myelopathy related to flexion of the neck characterized by progressive muscular weakness and atrophy of the distal upper limbs most frequently seen in young males. HD is thought to be secondary to an abnormal anterior displacement of the posterior dura with secondary compression of the lower cervical spinal cord and chronic injury to the anterior gray matter horns. We present two patients with HD and discuss its pathophysiology and imaging characteristics.

Author Biographies

Maria Catalina Vargas

Radiology Resident Department of Radiology, Fundacion Cardioinfantil – Instituto de Cardiologí­a

Mauricio Castlillo

Professor and Chief, Division of Neuroradiology

Department of Radiology, University of North Carolina at Chapel Hill

Diffusion restriction in thrombosed superior ophthalmic veins: Two cases of diverse etiology and literature review by Pendharkar et al.

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Published

2011-03-08

Issue

Vol. 5 No. 3 (2011)

Section

Neuroradiology

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