Coronary periarteritis in a patient with multi-organ IgG4-related disease

Authors

  • Yueyang Guo
  • David Ansdell
  • Sharon Brouha
  • Andrew Yen

DOI:

https://doi.org/10.3941/jrcr.v9i1.1967

Keywords:

immunoglobulin G4-related disease, coronary periarteritis, cardiac, computed tomography, PET

Abstract

Immunoglobulin G4-related disease is a recently described systemic clinicopathological entity characterized by immunoglobulin G4-producing plasmacytic infiltration of tissue and frequently by elevated serum immunoglobulin G4 concentration. Manifestations of this disease have been documented in nearly all organs and locations, but coronary artery involvement is not widely recognized. We report the coronary findings of a patient with multi-organ immunoglobulin G4-related disease. Non-electrocardiogram-gated computed tomography of the chest demonstrated nodular and rind-like periarterial soft tissue thickening along the proximal coronary artery segments with improvement following steroid therapy.

Published

2015-01-13

Issue

Section

Cardiac Imaging